Your Search for agammaglobulinemia matched 153 Documents (Page 1 of 6).
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Abstract: The clinical and neuroradiological findings of two patients with X-linked agammaglobulinemia, who developed a chronic encephalopathy, are presented. The main neurological manifestations in both patients were: progressive spastic tetraparesis, cortico-subcortical type of dementia an ...
http://www.aegis.org/aidsline/1994/mar/m9430553.html
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Abstract: We show that LPS-stimulated circulating CD14-positive monocytes from patients with common variable immunodeficiency (CVID) express a higher proportion of intracellular IL-12-positive cells than monocytes from patients with X-linked agammaglobulinemia or normal subjects. We used four-color flow cytometry and measured I ...
http://www.aegis.org/aidsline/2000/mar/a0030243.html
File Name: a0030243.html, Size: 11KB, Last Modified: Tuesday, March 28, 2000 at 8:12:04 PM
Abstract: OBJECTIVES: To determine the utility of single-stranded conformation polymorphism (SSCP) analysis for mutation screening in the ...
http://www.aegis.org/pubs/medline/1998/jan/m9811041.html
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Abstract: B cell precursors transiently express a pre-B cell receptor complex consisting of a rearranged mu heavy chain, a surrogate ligh ...
http://www.aegis.org/pubs/medline/1998/jan/m9811280.html
File Name: m9811280.html, Size: 6KB, Last Modified: Saturday, January 31, 1998 at 10:00:00 PM
Abstract: We have defined the clinical presentation and course of X-linked agammaglobulinemia (X-LA) by means of a multi-center retrospective survey of 96 patients. Infections were the most common presenting feature of patients with X-LA. The most frequent infections involved the upper respiratory tract (75%), lower respiratory ...
http://www.aegis.org/aidsline/1985/aug/m8580065.html
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Abstract: Alpha- and gamma-interferon (IFN) production by peripheral blood mononuclear cells (PBMC) from 18 patients affected by primary immunodeficiency syndromes was examined and compared with that of 20 normal donors. Patients included 8 with common variable immunodeficiency (CVI), 2 with congenital agammaglobulinemia, 4 wit ...
http://www.aegis.org/aidsline/1985/feb/m8520047.html
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Abstract: A series of monoclonal antibodies to T cell surface antigens were used to characterize peripheral lymphoid populations from patients with a variety of immunodeficiency diseases. Several disorders of T cell differentiation were observed to occur in severe combined immunodeficiency. One subtype of severe combined immuno ...
http://www.aegis.org/aidsline/1982/jan/m8210007.html
File Name: m8210007.html, Size: 10KB, Last Modified: Thursday, January 28, 1982 at 8:12:04 PM
Abstract: The X-linked lymphoproliferative syndrome (XLP) is characterized by a combined variable immunodeficiency with vulnerability to Epstein-Barr virus (EBV)-induced fatal or chronic infectious mononucleosis, acquired agammaglobulinemia, aplastic anemia, or malignant B cell lymphomas. Diagnosis of XLP requires documentation ...
http://www.aegis.org/aidsline/1981/jun/m8160004.html
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Abstract: Examples of human diseases that are characterized by abnormal immunoglobulin production and that appear to involve excessive or deficient T-helper and T-suppressor cell activities are discussed in this review. Among the primary disorders, diseases related to failure of T-cell help include abnormalities of blocks of T- ...
http://www.aegis.org/aidsline/1987/may/m8750346.html
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Abstract: T and B cell differentiation was examined in patients (pts) with common variable immunodeficiency (CVI, 16 pts), selective IgA deficiency (IgA-, 4 pts), X-linked agammaglobulinemia (XLA, 5 pts), and acquired immunodeficiency syndrome (AIDS, 5 pts) using monoclonal antibodies to four lymphocyte differentiation antigens ...
http://www.aegis.org/aidsline/1987/mar/m8730284.html
File Name: m8730284.html, Size: 10KB, Last Modified: Wednesday, January 07, 2009 at 5:05:04 AM
Abstract: The primary manifestation of the immunodeficiencies is undue susceptibility to infection. This means too many, too severe, too prolonged, too complicated and too unusual infections. Infections in immunodeficiency have a characteristic cause depending on the nature of the immune deficiency. Antibody deficiencies are as ...
http://www.aegis.org/aidsline/1986/oct/m86a0191.html
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Abstract: Viruses and bacteria in bronchoalveolar lavage fluids, protected specimen brush samples, and bronchial biopsies from 14 patients with primary hypogammaglobulinemia (11 patients with common variable immunodeficiency [CVID] and three patients with X-linked agammaglobulinemia [XLA]) were analyzed. At the time of the stud ...
http://www.aegis.org/aidsline/1999/jul/a9970503.html
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Abstract: BACKGROUND: We previously reported (New Engl J Med, 335:1431, 1996) that about 15% of HIV infected infants, who are more likely to develop rapid disease progression, have evidence of thymic dysfunction (TD+). More recently, we noted that TD+ infants who were infected in utero had the most rapid progression. It was of ...
http://www.aegis.org/aidsline/1998/dec/m98c3900.html
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Abstract: Sera from 77 patients with common variable immunodeficiency CVID) were tested for GB virus C (GBV-C) RNA, because they are prone to unexplained chronic hepatitis, and from 28 patients with X-linked agammaglobulinemia (XLA) who have a similar primary antibody deficiency but are not prone to hepatitis. Eight CVID and 8 ...
http://www.aegis.org/aidsline/1998/aug/m9880563.html
File Name: m9880563.html, Size: 9KB, Last Modified: Saturday, August 29, 1998 at 6:29:23 AM
Abstract: We investigated the presence of hepatitis C virus (HCV) infection in 58 patients with humoral immunodeficiencies. Forty-three of these patients had common variable immunodeficiency (CVI), 2 had sporadic hyperimmunoglobulin M (HIM) syndrome, 2 had immunoglobulin G subclass deficiency, 4 had ataxia-telangiectasia AT), a ...
http://www.aegis.org/aidsline/1997/jun/m9761174.html
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Abstract: The presence of hepatitis C virus (HCV) was investigated in 20 agammaglobulinemic patients using polymerase chain reaction (PCR) and by specific anti-HCV antibodies detection. Fourteen patients suffered from common variable immunodeficiency (CVID), 5 patients from X-linked agammaglobulinemia and one from specific anti ...
http://www.aegis.org/aidsline/1996/nov/m96b0846.html
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Abstract: The genetic defect associated with human X-linked agammaglobulinemia and murine X-linked immunodeficiency was recently shown to result from lack of function of a new cytoplasmic tyrosine kinase, called Bruton s tyrosine kinase (Btk). The phenotypes associated with these immunodeficiencies indicate that Btk plays a cri ...
http://www.aegis.org/aidsline/1995/feb/m9521020.html
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Abstract: We evaluated nine patients with humoral immunodeficiency (6 immunodeficiency with hyper-IgM, 2 X-linked agammaglobulinemia, 1 common variable immunodeficiency) who were being treated with intravenous immunoglobulins (IVIG). After the use of the IVIG regimen in a dose of 250-300 mg/kg/4 weeks for one year, the severity ...
http://www.aegis.org/aidsline/1993/oct/m93a0765.html
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Abstract: Chronically ill children who require life-long i.v. infusions in regular intervals (i.e. Agammaglobulinemia, HIV-infection) can be traumatized by such painful procedures. Some children gradually accept such infusions, whereas other children become sensitized and react with increasing fear and resistance. We report on ...
http://www.aegis.org/aidsline/1993/aug/m9380539.html
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Abstract: Congenital deficiencies that involve the lymphocyte system are complex and represent abnormalities in genetic control or gestational development. Only the more common prototypes of these diseases will be discussed. Diseases of the B cell system presented include X-linked agammaglobulinemia, selective IgA deficiency, I ...
http://www.aegis.org/aidsline/1991/sep/m9190529.html
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Abstract: Deficiencies of immune responsiveness can occur as either primary or secondary disorders. Secondary immunodeficiencies may be acquired as a consequence of treatment with immunosuppressive agents, nutritional deficiencies, and certain viral infections, the most notable of which is the HIV. Primary immunodeficiency dise ...
http://www.aegis.org/aidsline/1990/oct/m90a0680.html
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Abstract: The differentiation status of T and B cells was evaluated in patients with common variable immunodeficiency (CVI), selective IgA deficiency (IgA), X-linked agammaglobulinemia (XLA), and the acquired immune deficiency syndrome (AIDS) with the use of conventional lymphocyte markers and four new monoclonal antibodies tha ...
http://www.aegis.org/aidsline/1985/nov/m85b0135.html
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Abstract: Low levels of serum complement subcomponent C1q may accompany primary humoral immunodeficiency diseases such as sex-linked agammaglobulinemia, severe combined immunodeficiency, and common varied immunodeficiency. This selective depression of C1q is proportional to the degree of hypogammaglobulinemia, and is corrected ...
http://www.aegis.org/aidsline/1985/feb/m8520090.html
File Name: m8520090.html, Size: 9KB, Last Modified: Thursday, February 28, 1985 at 3:00:00 PM
Abstract: Partially inbred line UCD 140 chickens develop an age dependent inherited 7S immunoglobulin deficiency with features similar to acquired human agammaglobulinemia. Serial and developmental observations in line UCD 140 and control lines 440 and 444 reveal a significant progressive premature involution of the bursa of Fa ...
http://www.aegis.org/aidsline/1982/aug/m8280009.html
File Name: m8280009.html, Size: 9KB, Last Modified: Saturday, August 28, 1982 at 8:12:04 PM
Abstract: The immunopathogenesis of 25 kindreds affecting 100 males with the X-linked lymphoproliferative syndrome (XLP) is being studied comprehensively by our registry and laboratory group. XLP is a combined variable immune deficiency with Epstein-Barr virus (EBV) induced phenotypes of: (1) fatal infectious mononucleosis (IM) ...
http://www.aegis.org/aidsline/1982/may/m8250006.html
File Name: m8250006.html, Size: 11KB, Last Modified: Friday, May 28, 1982 at 8:12:04 PM
Abstract: Between January 1973 and September 1979, 2,092 horses and ponies were evaluated for immunologic disorders. A total of 418 abnormalities were detected in 416 (20%) of the animals tested. Disorders encountered were failure or partial failure of colostral immunoglobulin transfer from mare to foal (228 cases), combined im ...
http://www.aegis.org/aidsline/1981/mar/m8130003.html
File Name: m8130003.html, Size: 9KB, Last Modified: Saturday, March 28, 1981 at 8:12:04 PM
Abstract: The effect of different HIV-1 isolates on normal human B lymphocyte function has been studied in vitro. Production of IgM and IgG was measured by ELISA using a standard non-T preparation of B cells depleted of macrophages and T cells (but not of low-density accessory cells, LDC). Only one (H9/CBL-4) of five different ...
http://www.aegis.org/aidsline/1989/sep/m8990098.html
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Abstract: Immunoglobulin G subclass titers to three herpesviruses (herpes simplex; HSV; cytomegalovirus , CMV ; varicella zoster virus, VZV) were examined in patients with common variable immunodeficiency (CVI) before and after immunoglo ...
http://www.aegis.org/aidsline/1989/mar/m8930128.html
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Abstract: ...
http://www.aegis.org/aidsline/1989/jun/m8960390.html
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Abstract: ...
http://www.aegis.org/aidsline/1989/jun/m8960264.html
File Name: m8960264.html, Size: 8KB, Last Modified: Wednesday, January 07, 2009 at 5:26:36 AM